Cardiovascular magnetic resonance findings in a case of Danon disease

نویسندگان

  • Dorota Piotrowska-Kownacka
  • Lukasz Kownacki
  • Marek Kuch
  • Ewa Walczak
  • Agnieszka Kosieradzka
  • Anna Fidzianska
  • Leszek Krolicki
چکیده

Danon disease is a rare X-linked dominant lysosomal glycogen storage disease that can lead to severe ventricular hypertrophy and heart failure. We report a case of Danon disease with cardiac involvement evaluated with cardiovascular magnetic resonance, including late gadolinium enhancement and perfusion studies.

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عنوان ژورنال:
  • Journal of Cardiovascular Magnetic Resonance

دوره 11  شماره 

صفحات  -

تاریخ انتشار 2009